Tremor and Other Hyperkinetic Movements

A Case of Myoclonus–Dystonia Responding to Low-frequency Pallidal Stimulation

Harini Sarva, Joan Miravite, Matthew C. Swan, Andres Deik, Deborah Raymond, William L. Severt, Brian H. Kopell

Abstract


Background: High frequency pallidal stimulation has been shown to improve various types of dystonia, including myoclonus-dystonia.

Case Report: We report a case of epsilon sarcoglycan mutation-negative myoclonus-dystonia (MD) with response to low frequency bilateral pallidal stimulation.

Discussion: Low frequency pallidal stimulation provides an effective means of treating various dystonias, regardless of genetic status, as in our case, as it provides increased programming options with less adverse effects.



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